Har'a maloetse a tloaelehileng a bakoang ke phetoho ea liphatsa tsa lefutso, cystic fibrosis ea matšoafo e ka holimo ho lethathamong. Ts'oaetso ena e amahanngoa le ho tlōla ha sephiri se ngotsoeng ke litho tsa ka hare, tse lebisang ho hlōloa ha tsamaiso ea phefumoloho le pampiri ea meno.
Lefu la liphatsa tsa lefutso la cystic fibrosis
Lefu lena le potolohileng le boetse le bitsoa cystic fibrosis. E khetholloa ke lebelo le phahameng la viscosity ea mucus, e koahelang litho tsa sekoti. Ka lebaka la ts'ebetso ena, ho boloka liphiri ho fokotseha, 'me libaktheria tse ling tse bakang ho ruruha li atisa ho ata.
Cystic fibrosis ea matšoafo e na le sesosa se le seng - senya kromosome ea bosupa (letsoho le lelelele). Ho ea ka lipalo-palo, moetapele oa lefu lena ke motho e mong le e mong oa mashome a mabeli lefatšeng. Monyetla oa lefu lena ke 25%, hafeela batsoali ba babeli ba e-na le liphatsa tsa lefutso tse senyehileng.
Ho na le mefuta e meraro ea lefu lena:
- mala a motsoako oa cystic fibrosis;
- pulmonary kapa phefumoloho ea cystic fibrosis;
- mofuta o tsoakiloeng (pulmonary cystic fibrosis).
Cystic fibrosis ea matšoafo - matšoao
Lipontšo tse kholo tsa lefu lena:
- ho ba le sekhahla sa li-viscous, tse teteaneng nakong ea ho khohlela;
- ho eketseha hangata ha pneumonia, bronchitis, pneumonia;
- ho senya mala;
- ho tsoa ha metsi;
- bohloko, ho se utloise bohloko ka mpeng;
- ho ja lijo tse eketsehileng ka boima bo lekaneng le nts'etsopele ea 'mele;
- mathata a ho kopanela liphate;
- ho fokola ;
- ho bokella menoana matsohong;
- lefu la sebete;
- lefu la tsoekere;
- sinusitis ;
- ho fokola ha masapo;
- ho tsoa ha maleng (ho toba).
Mofuta oa cystic fibrosis oa pulmonary o iponahatsa lilemong tse peli tsa pele tsa bophelo, o khetholloa ka ho patala ha bohareng le ka hanyane ka hanyane ea ngoana.
Cystic Fibrosis - Tlhahlobo le Tlhahlobo
Ho hlahlojoa ho entsoe ka mekhoa e mene e ka sehloohong.
Ntlha ea pele, ho ba teng ha liphatsa tsa lefutso ho batsoali le liketsahalong tsa lelapa ho hlahlojoa. Litholoana tse ntle, hammoho le ho lemoha ha mekhoa e sa foleng ea ho ruruha matšoafong le bronchi, ho ba teng ha malapa a mala, ho fana ka mabaka a ho khanna mofufutso. E kenyeletsa ho lekanyetsa litekanyo tsa letsoai ka metsi a lokolitsoeng ke pores. E le ho etsa ts'ebetso ena, sebaka se senyenyane letsohong (ka holim'a setsoe) se tšoaroa ka lithethefatsi tse khethehileng tse bitsoang pilocarpine. Motlakase o kopantsoe sebakeng sena, ho etsa hore ho lokolloe ha mofufutso, o khetholloang ke polasetiki kapa mahlaseli a ho boloka mocheso, ho hlahisa phello ea sauna. Kamora metsotso e ka bang 40, metsi a hlahisoang a fumanoa ka letsoai. Haeba boemo ba eona bo feta meeli e thehiloeng, ho hlahlojoa ho qetela ho entsoe.
Cystic fibrosis ea phekolo ea matšoafo
Sebaka sa lefu lena ha se lumelle hore se phekole ka ho feletseng, phekolo e ikemiselitse ho felisa matšoao 'me e hloka mokhoa o kopanetsoeng. Kalafo e na le mesebetsi e latelang:
- lithupelo tse telele tsa lithibela-mafu;
- likolo tsa ho amoheloa ka mofuthu;
- kinesitherapy;
- Ho ruruha ha li-hormone tsa corticosteroid le beta mimetics;
- tšebeliso ea bronchodilator;
- ho etsa li-exercising tsa ho hema;
- ho lokisa lijo le ho eketseha ha tefo ea letsatsi ka letsatsi ka 10-15%;
- metsi a matšoafo a matšoafo;
- bug-massage;
- ho amohela li-vithamine le microelements.
E mahlahahlaha ebile e atlehile ka nakoana mokhoa oa phekolo ke lefu la ho transplant. Ho phaella moo, lipatlisiso tsa bongaka li ntse li etsoa ho lokisa liphatsa tsa lefutso tse senyehileng ka ho fetisisa ka likokoana-hloko tse entsoeng ka maiketsetso.