Lefu la Behcet

Lefu la Behcet ke boloetse bo sa foleng bo khutlang hape, lefu le tloaelehileng Japane le linaheng tsa Mediterranean. Hangata e hlaha ho batho ba lilemo li 30 ho isa ho tse 40. Lefu lena ke la vasculitis sehlopha 'me le na le etiology e sa tsejoeng.

Mabaka a Mafu a Behcet

Ts'ebetso ea lefu lena e amana le lintlha tse 'maloa tse khethollang, tse ling tse latelang:

Litsebi tse ngata li lumela hore ho qala ha lefu la Behçet ho bakoa ke lisosa tse tšoaetsanoang, 'me nakong e tlang, mekhoa ea boipheliso e itšetlehile ka bona, ho fanoe ka bolaoli ba lefutso.

Matšoao a lefu la Behcet ho basali

Lefu lena le khetholloa ke polysimptomicity. Tabeng ena, matšoao a ka sehloohong, ao u ka e fumanang ka ho nepahetseng, a amana le tšenyo ea liphatsa tsa lefutso tsa molomo le liphatsa tsa lefutso, hammoho le mekhoa ea ho ruruha mahlong. Nahana ka mehlala eohle ea lefu la Behçet ka botlalo.

Lipuo tsa molomo li senya

Qalong, liaparo tse nyenyane tse nang le litaba tse koahetsoeng ke marulelo li hlaha molomong, leholimong, lelemeng, marenene, pharynx, ka hare ho marameng, ao ka mor'a moo a bulehileng. Sebakeng sa li-vesicles, maqeba a pota-potileng (aphthae) a mmala a pinki a khanyang a thehoa, 'me boholo ba eona bo ka ba bophara ba 2 cm. Pholiso ea lisoathoa e etsahala hoo e ka bang khoeli hamorao, ka makhetlo a mararo ka selemo ho khutlela lithong.

Likokoana-hloko tsa malapa

Basali ka leseli le ka hare la botšehali le maqhubu a ba le liso, tse atisang ho ba bohloko, tse tšoanang le tse hlahang molomong. Ka mora ho folisa, litlolo li ka sala sebakeng sa tsona.

Mathata a pono

Lipontšo tsena li hlaha libeke tse 'maloa ka mor'a matšoao a molomong oa molomo. Mokuli a ka hlahisa ho ruruha ha 'mele oa iris le oa mahlo a mahlo, ho ruruha ha mesifa le maqeba a leihlo, ho ruruha ha cornea. Hangata ho na le matšoao a latelang: photophobia, pono e hlakileng, ho nyatsa ho eketsehileng.

Lipontšo tse nyenyane

Lintho tse sa tloaelehang tsa lipere, pyoderma, li-papulo-likokoana-hloko li ka bonahala. Hape maemong a mang, ho lahleheloa ke moriri oa lihlooho, subungual panaritium.

Mathata a tsamaiso ea mesifa

Ho na le ntshetsopele ea ramatiki (hangata lipheletsong tse tlaase) ntle le liketsahalo tse senyang.

Matšoao a li-neurological

Ho na le lintho tse ngata tse senyang methapo ea mafu, tlhahiso ea meningoencephalitis, edema ea optic methapo disk, ponahalo ea hemiparesis.

Liphetoho tse entsoeng ke ho ruruha ha maikutlo

Tšobotsi ea tsoelo-pele ea vasculitis, thrombophlebitis ea methapo ea maotong, thrombosis ea methapong e matla le thromboembolism ea pulmonary artery, aneurysm ea aortic, joalo-joalo.

Ka likokoana-hloko tsa pampiri, pelo le matšoafo, ho na le matšoao a joalo:

Kalafo ea Mafu a Behcet

Phekolo ea lefu la Behcet, pele ho tsohle, e reretsoe ho atolosa bophelo ba mokuli, ho finyella pholiso ea nako e telele le ho thibela liphetoho tse ke keng tsa fetoha likarolong tsa ka hare.

Matšoao a kotsi a Behcet's syndrome ka hara molomo le ka liphatsa tsa botona le botšehali a tlas'a phekolo ea moo ho sebelisoang glucocorticosteroids , tharollo ea likokoana-hloko, 'me ka linako tse ling - li-antipodal agents. Hape bakeng sa phekolo ea lefu lena, li-cytostatic agents, immunosuppressors, li-vithamine li ka boleloa. Tšenyo ea li-vascular e tšoaroa ke mekhoa ea ho buoa Bakuli ba bangata ba laeloa hore o hemorporal hemocorrection. Kalafo e etsoa tlas'a tlhokomelo ea kamehla ea bongaka.